The Journal of the Association of Physicians of Tamil Nadu Issue 1
A Rare Case of Congenital Cyanotic Heart Disease in Adult



The journal is published as a quarterly issue.
AUTHORS
HISTORY
Available Online: April 2020
ABSTRACT
Congenital heart diseases (CHD) in adults are uncommon. Especially Cyanotic CHDs (CCHD) in the adult is very rare. We had an adult patient with central cyanosis, pan-digital clubbing and systolic murmur over the left parasternal area. Assuming it to be a case of Tetralogy of Fallot (TOF), being the commonest with these features in adults, we admitted him. On detailed elicitation of the history, perusing his old records, and with fresh investigations, we diagnosed it to be a case of Double Outlet Right Ventricle (DORV) with pulmonary hypertension. On reviewing the literature, we found that DORV in children has a very poor prognosis; they do not usually survive to an adult unless operated1. Moreover, this patient had developed the typical complications “Paradoxical embolism” and “secondary polycythemia”. He had multiple cerebral abscesses with recurrent generalized convulsions.
KEYWORDS
DORV, Adult cyanotic heart disease, Paradoxical embolism, secondary polycythemia
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© 2020 Dr. Vijay Viswanathan, published by Association of Physicians of India-Tamilnadu State Chapter